Esplenomegalia El hiperesplenismo se caracteriza por: esplenomegalia. disminución de cifras de hematíes, leucocitos y plaquetas. Hiperesplenismo recurrente secundario a cardiomiopatia alcoholica despues de una anastomosis esplenorenal distal. Warren L. Garner. x. Warren L. Garner. vol número1 Hiperesplenismo secundario a compresión del eje esplenoportal por quiste hepático gigante Underwater hybrid endoscopic submucosal.

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In the present case, the need for a simultaneous pancreas and kidney transplant was based on the difficulty of diabetes control and problematic future scenario of adverse effects of immunosuppressors post-transplant due to chronic nephropathy.

The procedure was repeated approximately every cm until the duodeno-colonic anastomosis was reached. The mucosal surface is increased which results in an improved nutrient absorption. The gastrostomy tube output ranged from 2. With a follow-up of 24 months, the patient currently weighs 47 kg and leads a normal life. V fluids for the remaining time. In addition, the volume requirements were also reduced to less than half, with no negative impact on renal function.

At 12 months post-surgery, citrulline plasma level had increased to The patient underwent duodenal lengthening and tapering with 7 sequential transverse applications 5 of 45 mm and 2 of 60 mm of an endoscopic stapler on the anterior and posterior walls of the duodenum, respecting the pancreatic parenchyma and end-to-side duodeno-colonic anastomosis.

Splenectomy for splenomegaly and secondary hypersplenism

The main advantage of this new technique is that an additional intestinal absorptive surface is obtained without the need to discard any duodenal portion. Upper gastrointestinal series prior to the duodenal lengthening procedure showing the massively dilated duodenum ending in a stump. An enema showing a defunctionalized transverse colon from the hepatic flexure. This technique increases bowel length via the application of sequential stapling on alternating sides in a plane perpendicular to the long axis of the bowel.

Long-term follow-up of patients on home parenteral nutrition in Europe: Prior to surgery, he had a history of sexundario central-line infections and was colonized by multi-resistant Klebsiella pneumoniae. This increases the likelihood of achieving enteral autonomy while avoiding the need for intestinal transplantation 1 2.


The postoperative course was uneventful. J Am Coll Surg hipedesplenismo J Pediatr Surg ; To date, there are no reported experiences of duodenal lengthening in adults. He also follows an oral low-fiber diet ad libitum.

A gastrostomy tube was left in place to facilitate drainage of gastric and bilio-pancreatic secretions.

Duodenal lengthening may be effective as part of the autologous intestinal reconstruction armamentarium in adults with short bowel syndrome. Creatinine clearance has remained unchanged from that observed prior to surgery and the liver function test is normal.

The classical standard duodenal tapering technique reduces the luminal diameter of the dilated duodenum by removing its anti-pancreatic border longitudinally, usually with stapler devices 8. In the present case, the pre-lengthening citrulline level had increased from Similarly, the improvement in quality of life was questionable as the high gastrostomy output could result in a significant postoperative diarrhea following the establishment of the continuity of the intestinal tract.

Since these anatomical structures are situated inside the thickness of the pancreatic parenchyma, the risk of injury is circumvented by stapling the anterior and posterior aspects of the duodenum at a sufficient distance from the pancreas. The liver dysfunction was resolved via optimization of the parenteral formula. Intestinal transplant registry report: In addition, he was diagnosed with type 1 diabetes at the age of 4 and had already developed incipient nephropathy in the form of microalbuminuria.

We have demonstrated the feasibility of lengthening the duodenum via a modified version of the original STEP in a subset of children with SBS and a dilated duodenum 4.

Nevertheless, the use of intestinal transplantation has declined in recent years due to the associated high morbidity and mortality that lead to poorer survival than that seen in patients on home PN 5 6.

Upper gastrointestinal tract X-rays and barium enema demonstrated a dilated and elongated duodenum and a small-caliber defunctionalized colon, respectively Fig. Duodenal lengthening was performed with 7 sequential transverse applications 5 of 45 mm and 2 of 60 mm of an endoscopic stapler Endo GIA Stapler, Covidien LLC, Mansfield, MA, USA on the duodenal anterior and posterior walls, respecting swcundario pancreatic parenchyma as described elsewhere 4 Fig.


The next firing was similar from the opposite side, creating a duodenal channel 3 secundaroi in diameter.

A gastrostomy tube drained gastric and bilio-pancreatic secretions output range: Megaduodenum facilitates pyloric incompetence with alkaline reflux and dysmotility with stasis of intraluminal contents which sedundario result in bacterial overgrowth and malabsorption.

The lengthened duodenum measured 83 cm.


Although, the patient is able to successfully treat hypoglycemia episodes via the oral route. Its application in hiperrsplenismo has been reported in the literature 3.

July 27, ; Accepted: Postabsorptive plasma citrulline concentration is a marker of absorptive enterocyte mass and intestinal failure in humans. The third portion of the duodenum had been stapled, leaving a duodenal stump.

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An iterative mid-line incision was made under general anesthesia. The serial transverse enteroplasty procedure STEP is an intestinal lengthening procedure originally applied in pediatric patients with short bowel syndrome SBS and dilatation of the remnant small bowel. He is on a PN support volume of 1, ml and ml of I. Comparison of intestinal lengthening procedures for patients with short bowel syndrome. Therefore, whenever possible, autologous intestinal reconstruction should be considered before intestinal transplantation.

Surgical treatment at the time of the intestinal catastrophe consisted of the removal of the fourth part of the duodenum, the whole jejunum, ileon and ascending colon. The time required on a parenteral pump has shortened from the entire day to only 9 hours at night. The length of the retained duodenum measured from the pylorus was 30 cm.